Read ECG an important diagnostic test in cases of Duchene muscular dystrophy text version

ECG an important diagnostic test in cases of Duchenne muscular dystrophy

Muhammad Arif Khan, Abdullah AL -Jarallah Prince Salman Heart Centre, KFMC, RIYADH

Background

Duchene muscular dystrophy (DMD) Dilated cardiomyopathy Congestive cardiac failure Arrhythmias Sudden cardiac death

Background

ECG findings described in DMD

Short PR interval Long QTc Q waves RVH

American Journal of Cardiology Volume 103, Issue 2 , Pages 262-265, 15 January 2009 Re-examination of the Electrocardiogram in Boys With Duchenne Muscular Dystrophy and Correlation With Its Dilated Cardiomyopathy

Background

Two cases reported of Wolf Parkinson White Syndrome (WPW) associated with DMD

(Finsterer et al. Herz 2008)

We present a rare case to highlight the importance of ECG in DMD

Case Report

A 6 Years old boy with diagnosis of DMD since age of 4 years

ECG

Features of WPW syndrome: short PR interval < 0.01 sec positive delta wave in leads I, II, aVL, V4-6 negative delta waves in leads aVR & V1, prolonged QRS duration > 0.125 sec (NV 0.030.08)

Echocardiography

Normal LV size Normal LV function

ECHO, LAX

ECHO, M-Mode

Take home Messages

DMD is a progressive disease Ultimately leads to DCM WPW syndrome is a rare association ECG should be the part of routine cardiac evaluation in these patients EP management may be needed if patient become symptomatic

THANK YOU

ECG

American Journal of Cardiology Volume 103, Issue 2 , Pages 262-265, 15 January 2009 Re-examination of the Electrocardiogram in Boys With Duchenne Muscular Dystrophy and Correlation With Its Dilated Cardiomyopathy

Information

ECG an important diagnostic test in cases of Duchene muscular dystrophy

16 pages

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